Noninvasive ventilation (NIV) has been shown to improve daytime arterial blood gases and the symptoms associated with respiratory failure for neuromuscular disease patients.
In amyotrophic lateral sclerosis patients, NIV improves quality of life and sleep-related symptoms.
Bourke SC, et al. Noninvasive ventilation in ALS: Indications and effect on quality of life. Neurology 2003;
Eagle M, Bourke J, Bullock R, et al. Managing Duchenne muscular dystrophy—the additive effect of spinal surgery and home nocturnal ventilation in improving survival. Neuromuscular Disorders 2007;
Leger P, Bedicam JM, Cornette A et al. Nasal intermittent positive pressure ventilation. Long term follow up in patients with severe chronic respiratory insufficiency.